Neuropsychological Functioning in Children with Medium Chain Acyl Coenzyme A Dehydrogenase Deficiency (MCADD): The Impact of Early Diagnosis and Screening on Outcome

Children with medium chain acyl coenzyme A dehydrogenase deficiency (MCADD) have been reported to be at high risk for neurocognitive deficits. However this has not been systematically studied and little is known about the exact nature of neuropsychological sequelae or of the impact of early diagnosis and screening on outcome. We examined cognitive and adaptive outcome in children with MCADD (N?=?38, age range: 2 years, 2 months – 10 years, 3 months) diagnosed either through a newborn screening program (tandem mass spectrometry/MSMS) or upon clinical presentation. There was no evidence of overall intellectual impairment in either groups but there was some suggestion of poorer verbal and specific executive functioning (i.e., planning) abilities in the unscreened cohorts. Adaptive functioning was relatively intact with the exception of reduced Daily Living Skills in both our screened and unscreened groups. Early diagnosis and greater number of hospitalizations were related to higher verbal, communication, and socialization skills. Overall, our results highlight the importance of early diagnosis and management for children with MCADD.     

Reading and Spelling Disabilities in Children with and Without a History of Early Language Delay: A Neuropsychological and Linguistic Study

Language delay is a frequent antecedent of literacy problems, and both may be linked to phonological impairment. Studies on developmental dyslexia have led to contradictory results due to the heterogeneity of the pathological samples. The present study investigated whether Italian children with dyslexia showed selective phonological processing deficits or more widespread linguistic impairment and whether these deficits were associated with previous language delay. We chose 46 children with specific reading deficits and divided them into two groups based on whether they had language delay (LD) or not (NoLD). LD and NoLD children showed similar, severe deficits in reading and spelling decoding, but only LD children showed a moderate impairment in reading comprehension. LD children were more impaired in phonological working memory and phonological fluency, as well as in semantic fluency, grammatical comprehension, and verbal IQ. These findings indicate the presence of a moderate but widespread linguistic deficit (not limited to phonological processing) in a subset of dyslexic children with previous language delay that does not generalize to all children with reading difficulties.     

Executive function outcomes of children with traumatic brain injury sustained before three years

Traumatic brain injury (TBI) is a common cause of disability in childhood. While the outcomes of TBI sustained in school years has been heavily researched, very little is known about the impact of TBI in infants and young children. The aim of this study was to investigate the impact of TBI on executive function (EF) in children who sustained a TBI before 3 years of age. A group of 55 children, 19 with a mild TBI, 16 children with a moderate-severe TBI, and 20 uninjured comparison children participated. The EF of children aged 3 to 6 years were compared using child-based measures of attentional control and information processing. Parents completed questionnaires rating their child's EF. Severity groups differed on the child-based EF measure of attentional control with children with TBI performing below the control group. There were no significant group differences for information processing or parent-rated EF. It appears that children who sustain a TBI before the age of 3 years display impairments in some areas of attentional control 3–4 years postinjury. The findings fit with the existing EF literature for older children.     

Reformed church buildings in the Grand Duchy of Lithuania in the early-modern period*

Abstract

This article introduces the history of Reformed churches in the Grand Duchy of Lithuania. Against the backdrop of the history of the Reformation there, it discusses the cooperation between the Reformed and Lutherans, the response of the Counter-Reformation, and the history of the most important Lithuanian Reformed churches. It focuses on the nobility, especially the Radziwi?? family, the most important protectors of the Reformed. The family saw the Reformed faith as the key to the unity of the Grand Duchy, and an important way of strengthening the position of Lithuania vis-à-vis the Kingdom of Poland. They hoped that the Reformed faith could become the foundation of a sovereign Lithuanian state. As well as discussing the foundation and fate of Reformed communities in Vilnius and across Lithuania, the article also presents the first detailed account of the interiors and furnishings of their church buildings.     

From Latimer's Fellow-martyr to the ‘English Calvin': Nicholas Ridley's Reputation and the Circulation of A brief declaracion of the Lordes Supper, 1555-1570

Abstract

Nicholas Ridley, the Edwardian Bishop of London, was executed in 1555 during Mary Tudor's reign. An active publicist, he composed in prison a didactic treatise that promoted the Reformed view of the Eucharist and was published in Emden (1555) and in Strasbourg (1556). In 1556, A brief declaracion found its way to Geneva where a community of English exiles had it translated into Latin (Conrad Badius then issued a version in French). Not only did the translation acquire a polemical edge, but certain allusions, scattered in the preface and in the margins of the text, turned Ridley's treatise into a ‘Calvinist’ manifesto at a time when Calvin was ardently defending his views against the Lutheran polemicist, Westphal. Meanwhile, Jean Crespin made use of Badius's version in his martyrologies and reprinted Ridley's treatise in his 1570 edition. Whereas in England, Ridley's works began to be perceived as controversial after Mary's death, Crespin and Beza (Icones, 1580) kept his treatise alive and heralded him as the ‘English Calvin’ in French Reformed circles.     

The Anglican Covenant proposed by the Lambeth Commission 1

Abstract

The Lambeth Commission (2004) proposed a number of short-term and long-term solutions to issues raised by recent and highly controversial developments in the Episcopal Church (USA) and the diocese of New Westminster (Canada). From these events have emerged important questions about the nature of communion between, and the autonomy of, each of the 44 member churches of the Anglican Communion, and the way in which decisions of common concern are made. In order to consolidate this communion, as a long-term project, the Commission proposes the adoption of an Anglican Covenant by all 44 churches of the Communion. This article describes the terms of the proposed Covenant and identifies their provenance, in order to establish that the proposal is for the most part a restatement of classical Anglicanism. Only in serious cases of disagreement which substantially risk the unity of the Communion is the proposal innovative. The article also describes briefly reactions to and possible implementation of the proposed Covenant.     

From state church to faith community: an analysis of worldly and spiritual power in the Church of Sweden

The aim of this article is to discuss the current legislation, and power structures in and between different levels of the Church of Sweden in terms of church–state relations and secularisation, with the help of theories from sociology of religion and ecclesiology drawn from José Casanova, Grace Davie and Avery Dulles. With themes from Lutheran theology, including the two regiments and the common priesthood of all believers, we analyse the current legislation and power structures from the perspective of the so-called ‘dual line of responsibility’. The underlying hypothesis is that the structures of the former state church are still deciding the power structures in the Church of Sweden. This creates obscurity concerning the role of the church in public society and negatively affects the ecclesiastical development of the church now that it has lost its earlier status as a state church.     

Mother of God: A History of the Virgin Mary

Starting from the context in which there is an increasing emphasis on ecclesial revitalisation and churchplanting, the analytical model of the Australian National Church Life Survey (NCLS) research is introduced and described in its background and characteristics. The model shows particular interest in a specific church profile which is created based on local church surveys. The article describes the profile, examines the theological concepts and argues for in-depth empirical research in a Dutch context concerning the use of the profile.     

Community without memory? In search of an ecclesiology of liberation in the company of people with dementia

The increasing prevalence of dementia among members of the Christian Churches prompts a re-evaluation of Christian ecclesiology. This is particularly true for the ecclesiology born of the theologies of liberation, because of the emphasis it places upon conscious participation in the historical life of the community. The present article draws on stories of people with dementia as recorded by themselves and those close to them; by reflection upon these stories, it seeks to re-think the character of the Church in the face of this challenge, and so to offer a richer interpretation of its identity as a community of liberation.     

The Catholic Church,moral doctrine,and HIV prevention in Recife,Brazil: Negotiating the contradictions between religious belief and the realities of everyday life

Religious beliefs have had a key role in shaping local responses to HIV and AIDS. As the world's largest Catholic country, Brazil is no exception. Yet little research has been conducted to document how religious doctrine is enacted in practice among its lay leaders and followers. In this article, we present ethnographic research from Recife, Brazil, conducted to understand the way in which religious doctrines are interpreted at a local level. Contextualised within the sociology of contemporary Brazilian Catholicism, we draw on interviews with clergy members, lay leaders, and parishioners to discuss how the Catholic Church's vision of sexuality translates into everyday lives of its followers. We explore the disjuncture between the Catholic ideals of fidelity and delaying sex until marriage with the everyday reality of the Church's followers, highlighting the role that gender plays in defining sexual roles and expectations. We conclude by posing questions for future research and HIV prevention strategies considering the formal institutional response of the Brazilian Catholic Church to AIDS on the one hand, and the social and cultural contexts in which Catholics live their daily lives on the other.