MPS II: Adaptive Behavior of Patients and Impact on the Family System

Mucopolysaccharidosis type II (MPS II), also known as Hunter syndrome, is a chronic and progressive X-linked lysosomal disease that mainly affects males. It occurs in 1 in every 65,000 to 1 in 132,000 births. There are two distinct forms of the disease based on age of onset and clinical course: mild and severe. MPS II affects many organ systems including the nervous, cardiovascular, gastrointestinal and respiratory systems. Complications can include vision problems, progressive hearing loss, thickened and elastic skin, mental impairment, and enlarged liver and spleen. We herein focus on the adaptive behavior of individuals with MPS II, and the impact of MPS II on the family system. Outcomes from the Vineland-II Adaptive Behavior Scales showed that the MPS II patient sample experienced significantly lower functioning in communication, daily living skills, socialization, and motor skills compared to normative data. Patients with severe MPS II were found to have significantly lower adaptive functioning in all domains, as compared to those with mild MPS II. Length of time on ERT had no significant relationship to adaptive functioning. Results from the Peds QL Family Impact Module indicated that families of patients with MPS II experienced a lower overall health-related quality of life and overall lower family functioning (including lower emotional and cognitive functioning) than those with chronic illnesses residing in an inpatient setting.     

An experiential thinking style: its facets and relations with objective and subjective criterion measures

In Study 1, an experiential factor divided into the following 3 factors when 3 or more factors were extracted: intuition, emotionality, and imagination; whereas a rational factor retained its coherence. In Study 2, an experiential but not a rational thinking style was positively associated with performance measures of creativity, humor, aesthetic judgment, and intuition and with self-report measures of empathy and social popularity. A rational thinking style was associated with several measures of adjustment. Both thinking styles were positively related to personal growth. Support was provided from several sources for the discriminant validity of the experiential facets. In a third study, the independence of the 2 thinking styles and of gender differences in self-reported data were verified by observations by others of participants' thinking styles. The importance of identifying facets of an experiential thinking style and of discovering previously unrecognized favorable attributes of this thinking style was discussed.     

Imprisoning masculinity

Prisons are characterized by a hierarchical and antagonistic institutional culture. The processes of the managerial and work culture in violent organizations, such as the prison, incorporate an explicit focus on authority and compliance with rigid rules and procedures; in this context, difference attracts harassment and victimization. These processes also encompass the enactment of “ordinary” authority, the normalization of harassment, and the ways in which violence is embedded in routine conversations and explanations (Hearn, 1996; 55). Group relations can function to legitimize, socialize and reproduce the values and practices connected with violence (Morgan, 1987: 185). Thus a focus on peer group relations, between and within groups of officers and prisoners, is critical and may reveal that which we would rather not know: that the functioning of prisons may be actively and significantly counterproductive to their proclaimed task—the reduction of crime.     

Indclas: A three-way hierarchical classes model

A three-way three-mode extension of De Boeck and Rosenberg's (1988) two-way two-mode hierarchical classes model is presented for the analysis of individual differences in binary object × attribute arrays. In line with the two-way hierarchical classes model, the three-way extension represents both the association relation among the three modes and the set-theoretical relations among the elements of each model. An algorithm for fitting the model is presented and evaluated in a simulation study. The model is illustrated with data on psychiatric diagnosis. Finally, the relation between the model and extant models for three-way data is discussed.The research reported in this paper was partially supported by NATO (Grant CRG.921321 to Iven Van Mechelen and Seymour Rosenberg).     

Relationship Between Race and Attitudes Toward Black Men

This article presents an empirical method for assessing attitudes toward Black men. The findings document that race is a significant factor in determining how Black men are perceived by Black and White college students.     

Use of dialectical psychotherapy in treating bulimarexic disorders: A case study

A variety of therapeutic approaches have been used in the treatment of anorexia nervosa and bulimia with varying degrees of success. This paper describes the treatment of a bulimarexic patient by co-therapists, using a dialectical approach.Appreciation is extended to Betty Hoffman for her editorial assistance.     

VALUES MOTHERS HOLD FOR HANDICAPPED AND NONHANDICAPPED PRESCHOOL CHILDREN IN JAPAN,PUERTO RICO,AND THE UNITED STATES MAINLAND*

This study examines the values held by mothers in Japan, Puerto Rico and the U.S. Mainland for their handicapped and nonhandicapped preschoolers in the contexts of home and school. In order to study values, mothers from the three cultures were asked to rank twelve value items relating to four value areas: physical, intrapersonal, interpersonal, and sociocultural. The value rankings were different in the three cultures and depended upon the home and school contexts. The presence of a diagnosed orthopedic and/or neurological impairment in the child had no overall effect on value ratings but did interact with culture and context to influence mothers' values.