Young Adults with MSUD and Their Transition to Adulthood: Psychosocial Issues

Maple Syrup Urine Disease (MSUD) is an autosomal recessive condition with an incidence of 1 in 185,000 births worldwide. Regardless of the type of MSUD, treatment includes immediate and lifelong dietary restriction of isoleucine, leucine and valine. There is little known about the psychosocial impact of MSUD on the developmental milestones of emerging adulthood. We used a qualitative case study approach to explore the human experiences of MSUD on young adults (n?=?8) and parents (n?=?8). All participants were administered a semi-structured, qualitative interview as well as quantitative measures. Six core themes emerged: 1) lifelong strain of dietary management; 2) social isolation from peers and impact on dating; 3) impact of MSUD on academics and employment; 4) medical experiences and transition to adult care; 5) impact on family functioning; and 6) positive effects and growth. The results of this investigation highlight and expand awareness of the psychological and social needs of young adults with MSUD. This study calls for a collaborative, multidisciplinary effort in the treatment of these patients and their families.     

Profiles of emotion regulation: Understanding regulatory patterns and the implications for posttraumatic stress

Trauma survivors often experience posttraumatic stress (PTS) and report concurrent difficulties with emotion regulation (ER). Although individuals typically use multiple regulatory strategies to manage emotion, no studies yet examine the influence of a constellation of strategies on PTS in a community sample. We assessed six ER strategies and investigated whether specific profiles of ER (i.e. the typical pattern of regulation, determined by how often each strategy is used) were related to PTS. A hierarchical cluster analysis indicated that four distinct profiles were present: Adaptive Regulation, Active Regulation, Detached Regulation, and Maladaptive Regulation. Further analyses revealed that an individual's profile was not related to frequency of past trauma, but had the power to differentiate symptom severity for overall PTS and each symptom cluster of posttraumatic stress disorder. These findings highlight how profiles characterising multiple regulatory strategies offer a more complete understanding of the ways ER can account for PTS.     

Dehumanizing but competent: The impact of gender,illness type,and emotional expressiveness on patient perceptions of doctors

This study is the first attempt to investigate men's and women's anticipated reactions to a consultation with a doctor holding either a dehumanizing or humanistic approach to patient treatment. Participants (N = 375) read a vignette depicting a doctor's treatment philosophy—emphasizing either the metaphor of the body as a machine (dehumanizing condition) or emphasizing individual humanness (humanizing condition). They then imagined consulting the doctor about a psychological or physical illness. Although, medical dehumanization had undesirable consequences, some men rated the dehumanizing doctor as more competent than the humanizing doctor. These were men who were (a) emotionally expressive and seeking help for a psychological illness, and (b) men low in emotional expressiveness seeking help for a physical illness.     

Met expectations: The effects of expected and delivered inducements on employee satisfaction

Interpretation of existing theory and research on met expectations is problematic due to ambiguous conceptualization of the met expectations hypothesis and limitations imposed by the measurement strategies typically employed in this domain (i.e. difference scores and direct retrospective measures). In this longitudinal study, we sought to overcome these problems by using an alternative methodology to conduct a more comprehensive test of the met expectations hypothesis based on Warr's (1987) Vitamin Model and on research in related fields (e.g. person–environment fit). Polynomial regression and response surface analyses were used to examine how employee satisfaction is related to unmet, met, and exceeded expectations concerning two distinct types of inducements analogous to vitamins A (skill development opportunities) and E (support, compensation). Respondents included 342 limited term employees. Consistent with previous research, our results indicated that unmet expectations of any sort were associated with decreased satisfaction. However, contrary to common interpretations of the extant literature, our results also indicated that met expectations were not always associated with high levels of satisfaction and that exceeded expectations were, in the case of skill development, negatively associated with satisfaction. These findings suggest a need to broaden existing met expectations theory and to refine common organizational practices.     

Contextual information and memory for unfamiliar tunes in older and younger adults

We examined age differences in the effectiveness of multiple repetitions and providing associative facts on tune memory. For both tune and fact recognition, three presentations were beneficial. Age was irrelevant in fact recognition, but older adults were less successful than younger in tune recognition. The associative fact did not affect young adults' performance. Among older people, the neutral association harmed performance; the emotional fact mitigated performance back to baseline. Young adults seemed to rely solely on procedural memory, or repetition, to learn tunes. Older adults benefitted by using emotional associative information to counteract memory burdens imposed by neutral associative information.     

A further refinement of procedures addressing food selectivity

Individuals with autism and/or developmental disabilities are more likely than their typically developing peers to be food selective. Evidence‐based treatment packages for food refusal and selectivity include the use of reinforcement, escape extinction, and manipulation of antecedent events . In the current study, the variety of foods consumed by two adolescent males with food selectivity were systematically increased to include a variety of foods across all of the food groups. A changing criterion design was used to systematically increase the expectation of the amount and variety of foods that were consumed.     

Are three-sample tasks less sensitive than two-sample tasks? Memory effects in the testing of taste discrimination

In order to provide insights into why discrimination protocols with three stimuli sometimes tend to be less sensitive than protocols with two stimuli, two experiments were conducted. In these experiments, the relative effects of memory decay and memory interference were investigated. Both experiments involved purified water and/or solutions of low NaCl concentration. In Experiment 1, three protocols were compared: the traditional same-different test (Protocol 1), the same protocol with a rinse between the two samples (Protocol 2), and Protocol 2 with an added time delay between the first sample and the intermediate rinse (Protocol 3.) The decrease in measured d' values as time delay increased indicated that memory decay might be a factor for tests with three stimuli, such as the triangle method, rendering it less sensitive than tests with two stimuli, such as the same-different method. In Experiment 2, four protocols were compared: the traditional same-different test, the two-rinse same-different test, the triangle test, and what will be called duo same-different test. The experimental design allowed the individual consideration of memory decay and interference effects. From this last experiment, the substantial effect of memory interference was uncovered. Further experimentation will be necessary to estimate the exact relative effects of memory interference and memory decay.