Neuropsychological Functioning in Children with Medium Chain Acyl Coenzyme A Dehydrogenase Deficiency (MCADD): The Impact of Early Diagnosis and Screening on Outcome

Children with medium chain acyl coenzyme A dehydrogenase deficiency (MCADD) have been reported to be at high risk for neurocognitive deficits. However this has not been systematically studied and little is known about the exact nature of neuropsychological sequelae or of the impact of early diagnosis and screening on outcome. We examined cognitive and adaptive outcome in children with MCADD (N?=?38, age range: 2 years, 2 months – 10 years, 3 months) diagnosed either through a newborn screening program (tandem mass spectrometry/MSMS) or upon clinical presentation. There was no evidence of overall intellectual impairment in either groups but there was some suggestion of poorer verbal and specific executive functioning (i.e., planning) abilities in the unscreened cohorts. Adaptive functioning was relatively intact with the exception of reduced Daily Living Skills in both our screened and unscreened groups. Early diagnosis and greater number of hospitalizations were related to higher verbal, communication, and socialization skills. Overall, our results highlight the importance of early diagnosis and management for children with MCADD.     

Wisconsin card sorting test and Halstead Category Test performances of children and adolescents who exhibit the syndrome of nonverbal learning disabilities

Abstract

Wisconsin Card Sorting Test (WCST) and Halstead Category Test (HCT) performances of 15 children/adolescents (age range 9 to 17 years) diagnosed with the syndrome of nonverbal learning disabilities (NLD) and 15 age-, gender-, and FSIQ-matched verbal learning-disabled (VLD) controls were examined. The VLD group made significantly fewer errors on the HCT than did the NLD group. In addition, the VLD controls significantly outperformed the NLD participants on seven of the nine WCST index scores (all except failure to maintain set and learning to learn scores). Consistent with the adult literature, the common variance between the HCT and WCST was modest, indicating that these two neuropsychological measures gauge different domains of functioning. It is suggested that the HCT assesses conceptualization/higher order reasoning abilities, whereas the WCST taps dimensions of executive functioning.     

How Children Learn the Ins and Outs: A Training Study of Toddlers' Categorization of Animals

Young children are able to categorize animals on the basis of unobservable features such as shared biological properties (e.g., bones). For the most part, children learn about these properties through explicit verbalizations from others. The present study examined how such input impacts children's learning about the properties of categories. In a training study with thirty-six 2.5-year-olds (M_age = 2;9), we tested the prediction that a relatively small amount of input highlighting the importance of unobservable properties would lead to a gradual shift in children's use of these properties for categorization. Children with no initial categorization bias were trained to categorize either on the basis of shared unobservable properties or shared observable properties. During 3 days of training, children gradually developed a categorization bias in the direction of the property type for which they received training and sustained this bias more than a week after training. Also, a set of children who exhibited an initial perceptual bias showed an abrupt change in how they categorized after only 1 training session.     

First Impressions: Exploring the Structure of Titles for Nonformal Public Interpretive Programs

ABSTRACT

Visitors considering attending an interpretive program open to the public at a zoo, historic site, park, or museum may have no more information available to them than the title of the program and its location and date. This research investigated how the structure of a program title helped or hindered people from inferring the topic of the program, whether it is for adults or children, level of formality, and interestingness. Ninety-six college students at 2 universities rated 18 titles for interpretive programs on 4 dimensions. Interestingness of the program topic was related to reported intention to attend the program. Being able to infer whether the program was for adults or children and whether it was formal or informal was related to interestingness. Program titles should be strategically constructed as potential program participants make inferences about the program from the title.     

Interpersonal constructs and communicative ability in a police environment: A preliminary investigation

Abstract

This study investigates the relation between indexes of the development of interpersonal construct systems and the qualities of messages generated in response to persuasive tasks within the context of an urban police force. Hypotheses assuming that length of service as a line officer would predict less developed construct systems, and that more developed construct systems would predict message strategies that acknowledge the unique qualities of receivers found general support. In addition, the possibility of further relations between length of service and message variables was explored, but no substantial evidence was found for such effects. These results show the importance of environmental influences on construct development, and suggest that interpersonal perception and message behavior functionally adapt to the needs of organizational participation.     

A validation study of Belbin's team roles

The Belbin team role preferences of the members of 55 teams were assessed by three independent methods: (1) Cattell's 16PF (Form 5) personality questionnaire, (2) video observation of a business simulation exercise and subsequent analysis with a Belbin behavioural checklist, and (3) Saville and Holdsworth's Occupational Personality Questionnaire. The 338 participants were drawn in approximately equal measure from managerial and non-managerial levels from equal numbers of manufacturing and public service organizations. A multitrait-multimethod correlation matrix derived from the data collected from the participants was employed to evaluate the convergent and discriminant validities of the Belbin team roles. Application of the Campbell and Fiske criteria to the matrix did not produce clear support for discriminant validity. Application of a correlated uniqueness model in a confirmatory factor analysis showed the Belbin team role model to be overparameterized and to lack both convergent and discriminant validity. Further modelling revealed that the Belbin team roles fit easily into a “Big Five” five-factor personality framework.     

The journey of gestational surrogacy: religion,spirituality and assisted reproductive technologies

This article discusses the intersection of women’s experiences with the assisted reproductive technological practice of gestational surrogacy and spirituality and religion. During the interviews of eight gestational surrogates themes of spirituality-, religion- and faith-based language emerged as these women shared their narratives of assisted reproductive technologies in this Canadian study. Professionals supporting women before, during and after the experience of gestational surrogacy need to be mindful of the significance of spirituality and religion in third party reproduction practices for many women. In discussing these topics with gestational surrogates counsellors, child and youth care practitioners, faith leaders, social workers, and educators need to remain open and attentive to a multiplicity of diverse theological negotiations.     

Assessing spiritual well-being: relating with God explains greatest variance in spiritual well-being among Australian youth

How do we set standards in assessing spiritual well-being (SWB)? Most measures provide only scores on arbitrary scales. Therefore, if the questions differ, the scores are likely to as well. This paper reports on two scales developed with 460 Australian secondary school students, with diverse cultural and religious backgrounds, from state, Catholic, Christian Community and independent schools. The four domains model of spiritual health/well-being was the theoretical base from which 12 items were developed to reflect quality of relationships with each of self, others, environment and God/the Divine. The instrument with the five top-scoring items in each domain, known as Spiritual Health And Life-Orientation Measure (SHALOM), has been sought for use in over 200 studies in 20 languages. The second-highest sets of five items were extracted and found to form statistically valid factors, for a new instrument called SWBQ2. As would be expected, the mean values for the factor scores varied between SHALOM and SWBQ2, overall and by school type. However, regression analyses of the lived experience scores showed that relating with God provided greatest explanation of variance in SWB, on both measures. A double-response method introduced for SHALOM was also used with SWBQ2 to compare each person’s lived experience with their ideals, better reflecting quality of relationships, rather than just the arbitrary scores. There was negligible difference in dissonance scores on the four factors in both measures, that is, in comparing the difference between ideals and lived experiences. This method showed consistency in the quality of relationships reflecting SWB, contrasted with variance shown using only lived experience, as mentioned above. Relating with God was again most influential on SWB. These findings have implications for methods used in assessing SWB as well as outcomes.     

Sweetening the Till: The Use of Candy to Increase Restaurant Tipping1

A common practice among servers in restaurants is to give their dining parties an unexpected gift in the form of candy when delivering the check. Two experiments were conducted to evaluate the impact of this gesture on the tip percentages received by servers. Experiment 1 found that customers who received a small piece of chocolate along with the check tipped more than did customers who received no candy. Experiment 2 found that tips varied with the amount of the candy given to the customers as well as with the manner in which it was offered. It is argued that reciprocity is a stronger explanation for these findings than either impression management or the good mood effect.